GLB1, NT (GLB1, ELNR1, Beta-galactosidase, Acid beta-galactosidase, Elastin receptor 1)

This webpage contains legacy information. The product is either no longer available from the supplier or has been delisted at Labome.

product summary

company name :

US Biological

product type :

antibody

product name :

GLB1, NT (GLB1, ELNR1, Beta-galactosidase, Acid beta-galactosidase, Elastin receptor 1)

catalog :

036066

quantity :

200 ul

clonality :

polyclonal

host :

domestic rabbit

conjugate :

nonconjugated

reactivity :

human

product information

Catalog Number :

036066

Product wo Prefix :

GLB1, NT (GLB1, ELNR1, Beta-galactosidase, Acid beta-galactosidase, Elastin receptor 1)

Host :

rabbit

Product Type :

Pab

Category :

Antibodies

Size1 :

200 ul

Isotype :

IgG

Desc1 :

This gene encodes beta-galactosidase-1, a lysosomal enzyme that hydrolyzes the terminal beta-galactose from ganglioside substrates and other glycoconjugates. Defects in this gene are the cause of GM1-gangliosidosis and Morquio B syndrome. Multiple transcript variants encoding different isoforms have been found for this gene. Applications: Suitable for use in Western Blot, ELISA Recommended Dilution: ELISA: 1:1,000 Western Blot: 1:100-500 Storage and Stability: May be stored at 4°C for short-term only. Aliquot to avoid repeated freezing and thawing. Store at -20°C. Aliquots are stable for 12 months. For maximum recovery of product, centrifuge the original vial after thawing and prior to removing the cap.

Calc Crossreactivity :

Alternate Name :

GLB1, ELNR1, Beta-galactosidase, Acid beta-galactosidase, Elastin receptor 1

Immunogen :

GLB1 antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 80-109 amino acids from the N-terminal region of human GLB1.

Specificity :

Human

Purity :

Purified by Protein A affinity chromatography.

Form :

Supplied as a liquid in PBS, pH 7.2, 0.09% sodium azide.

Concentration :

As reported

Desc2 :

Product Type: Pab Isotype: IgG Host: rabbit Source: human Concentration: As reported Form: Supplied as a liquid in PBS, pH 7.2, 0.09% sodium azide. Purity: Purified by Protein A affinity chromatography. Immunogen: GLB1 antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 80-109 amino acids from the N-terminal region of human GLB1. Specificity: Human Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications without the expressed written authorization of United States Biological.

Calc Applications Abbrev :

E WB

Storage Temperature :

-20°C

Reference :

Rose, J.E., et al. Mol. Med. 16 (7-8), 247-253 (2010) : Dubois, P.C., et al. Nat. Genet. 42(4):295-302(2010) Antonicelli, F., et al. Wound Repair Regen 17(5):631-638(2009) Hofer, D., et al. Hum. Mutat. 30(8):1214-1221(2009) Mayer, F.Q., et al. Mol. Genet. Metab. 96 (3), 148 (2009) :

Picture 1 File Name :

https://usbio-images.r.worldssl.net/prodimages/48/036066_1.jpg