PMPCA Antibody - BSA Free | Novus Biologicals NBP1-89126 product information

product summary

company name :

Novus Biologicals

other brands :

IMGENEX

product type :

antibody

product name :

PMPCA Antibody - BSA Free

catalog :

NBP1-89126

quantity :

0.1 ml (also 25 ul)

price :

499 USD

clonality :

polyclonal

host :

domestic rabbit

conjugate :

nonconjugated

reactivity :

human

application :

western blot, immunohistochemistry, immunocytochemistry, immunohistochemistry - paraffin section

more info or order :

Novus Biologicals product webpage

citations: 5

Reference
Rambani V, Kolnikova M, Cagalinec M, Skopková M, Gasperikova D. PMPCA-Related Encephalopathy: Novel Variants, Phenotype Extension, and Mitochondrial Morphology. Neurol Genet. 2023;9:e200106 pubmed publisher
Charif M, Chevrollier A, Gueguen N, Kane S, Bris C, Gouden xe8 ge D, et al. Next-Generation Sequencing Identifies Novel PMPCA Variants in Patients with Late-Onset Dominant Optic Atrophy. Genes (Basel). 2022;13: pubmed publisher
Moes A, Severs D, Verdonk K, van der Lubbe N, Zietse R, Danser A, et al. Mycophenolate Mofetil Attenuates DOCA-Salt Hypertension: Effects on Vascular Tone. Front Physiol. 2018;9:578 pubmed publisher
Joshi M, Anselm I, Shi J, Bale T, Towne M, Schmitz Abe K, et al. Mutations in the substrate binding glycine-rich loop of the mitochondrial processing peptidase-α protein (PMPCA) cause a severe mitochondrial disease. Cold Spring Harb Mol Case Stud. 2016;2:a000786 pubmed publisher
Jobling R, Assoum M, Gakh O, Blaser S, Raiman J, Mignot C, et al. PMPCA mutations cause abnormal mitochondrial protein processing in patients with non-progressive cerebellar ataxia. Brain. 2015;138:1505-17 pubmed publisher

product information

master code :

NBP1-89126

SKU :

NBP1-89126

product name :

PMPCA Antibody - BSA Free

unit size :

0.1 ml (also 25 ul)

description :

The PMPCA Antibody - BSA Free from Novus is a rabbit polyclonal antibody to PMPCA. This antibody reacts with human. The PMPCA Antibody - BSA Free has been validated for the following applications: Western Blot,Immunocytochemistry/ Immunofluorescence,Immunohistochemistry,Immunohistochemistry-Paraffin,Knockdown Validated.

target :

PMPCA

category :

Primary Antibodies

buffer :

PBS (pH 7.2) and 40% Glycerol

clonality :

Polyclonal

conjugate :

Unconjugated

host :

Rabbit

immunogen :

VEHEHLVDCARKYLLGVQPAWGSAEAVDIDRSVAQYTGG
IAKLERDMSNVSLGPTPIPELTHIMVGLESCSFLEEDFI
PFAVLNMMMGGGGSFSAGGPGKGMFSR
This antibody was developed against Recombinant Protein corresponding to amino acids:

isotype :

IgG

purity :

Immunogen affinity purified

species :

Human

gene symbol :

PMPCA

Antibody validation :

Independent Anitbodies

applications :

Western Blot,Immunocytochemistry/ Immunofluorescence,Immunohistochemistry,Immunohistochemistry-Paraffin,Knockdown Validated

USD :

499 USD

alt names :

Alpha-MPPMGC104197, EC 3.4.24.64, inositol polyphosphate-5-phosphatase, 72 kD, INPP5E, KIAA0123FLJ26258, mitochondrial matrix processing protease, alpha subunit, mitochondrial-processing peptidase subunit alpha, MPPA, P-55, peptidase (mitochondrial processing) alpha

storage :

Store at 4C short term. Aliquot and store at -20C long term. Avoid freeze-thaw cycles.

more info or order :

Novus Biologicals product webpage