product summary
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company name :
MyBioSource
product type :
ELISA/assay
product name :
Rat Fumarylacetoacetase, FAH ELISA Kit
catalog :
MBS9331000
quantity :
48-Strip-Wells
price :
435 USD
more info or order :
MyBioSource product webpage
product information
catalog number :
MBS9331000
products type :
ELISA Kit
products full name :
Rat Fumarylacetoacetase, FAH ELISA Kit
products short name :
fumarylacetoacetate hydrolase (fumarylacetoacetase)
products name syn :
Rat Fumarylacetoacetase (FAH) ELISA kit; OTTHUMP00000185572; fumarylacetoacetase; fumarylacetoacetate hydrolase (fumarylacetoacetase)
other names :
fumarylacetoacetase; Fumarylacetoacetase; fumarylacetoacetase; FAA; beta-diketonase; fumarylacetoacetate hydrolase; Beta-diketonase; Fumarylacetoacetate hydrolase
products gene name :
FAH
other gene names :
Fah; Fah; FAA
uniprot entry name :
FAAA_RAT
reactivity :
Rat
specificity :
No significant cross-reactivity or interference between this analyte and analogues is observed.
storage stability :
Store all reagents at 2-8 degree C
other info1 :
Samples: Serum, Plasma and Tissue Homogenate. Assay Type: Sandwich. Detection Range: 0.25 ng/ml - 8 ng/ml. Sensitivity: 0.1 ng/ml.
other info2 :
Intra-assay Precision: Intra-assay CV (%) is less than 15%. Inter-assay Precision: Inter-assay CV (%) is less than 15%. [CV(%) = SD/mean ×100].
products description :
Background: This Quantitative Sandwich ELISA kit is only for in vitro research use only, not for drug, household, therapeutic or diagnostic applications! This kit is intended to be used for determination the level of FAH (hereafter termed this analyte) in Rat serum, plasma and tissue homogenate samples.
ncbi gi num :
8393349
ncbi acc num :
NP_058877.1
ncbi gb acc num :
NM_017181.2
uniprot acc num :
P25093
ncbi mol weight :
45,976 Da
ncbi pathways :
Metabolism Pathway (573935); Metabolism Of Amino Acids And Derivatives Pathway (574057); Phenylalanine And Tyrosine Catabolism Pathway (574062); Tyrosine Degradation, Tyrosine = Homogentisate Pathway (522682); Tyrosine Degradation, Tyrosine = Homogentisate Pathway (468237); Tyrosine Metabolism Pathway (83351); Tyrosine Metabolism Pathway (325)
ncbi summary :
deficiency leads to human hereditary tyrosinemia type 1 [RGD, Feb 2006]
uniprot summary :
FAH: Defects in FAH are the cause of tyrosinemia type 1 (TYRO1). An inborn error of metabolism characterized by elevations of tyrosine in the blood and urine, and hepatorenal manifestations. Typical features include hepatic necrosis, renal tubular injury, episodic weakness, self-mutilation, and seizures. Renal tubular dysfunction is associated with phosphate loss and hypophosphataemic rickets. Progressive liver disease can lead to the development of hepatocellular carcinoma. Dietary treatment with restriction of tyrosine and phenylalanine alleviates the rickets, but liver transplantation has so far been the only definite treatment. Belongs to the FAH family. Protein type: EC 3.7.1.2; Amino Acid Metabolism - tyrosine; Hydrolase. Molecular Function: fumarylacetoacetase activity; metal ion binding. Biological Process: L-phenylalanine catabolic process; tyrosine catabolic process; aromatic amino acid family metabolic process; arginine catabolic process
size1 :
48-Strip-Wells
price1 :
435 USD
size2 :
96-Strip-Wells
price2 :
600
more info or order :
MyBioSource product webpage
company information
MyBioSource
P.O. Box 153308
San Diego, CA 92195-3308
sales@mybiosource.com
https://www.mybiosource.com
1-888-627-0165
headquarters: USA
MyBioSource, LLC was orginally founded in Vancouver by three enthusiastic scientists who are passionate about providing the world with the best reagents available. Together, they form a company with a big vision known as MyBioSource. MyBioSource is now located in San Diego, California, USA.

"MyBioSource's number 1 vision is to be the world's number 1 quality reagents provider."

Our goal is to provide researchers, scientists and customers alike with a one-stop-shop for all of their reagents needs, whether it is monoclonal antibody, polyclonal antibody, recombinant protein, peptide, etc...

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