product summary
Loading...
company name :
MyBioSource
product type :
antibody
product name :
HCCS Antibody
catalog :
MBS7043915
quantity :
0.05 mL
price :
120 USD
clonality :
polyclonal
host :
rabbit
conjugate :
nonconjugated
reactivity :
human, mouse
application :
western blot, ELISA, enzyme immunoassay
more info or order :
image
image 1 :
Western blot. All lanes: HCCS antibody at 3.54 ug/ml. Lane 1: Mouse small intestine tissue. Lane 2: Human placenta tissue. Lane 3: Mouse kidney tissue. Lane 4: Mouse heart tissue. Lane 5: Mouse skeletal muscle tissue. Lane 6: Hela whole cell lysate. Lane 7: Raw264.7 whole cell lysate. Lane 8: MCF7 whole cell lysate. Lane 9: HepG-2 whole cell lysate. Secondary. Goat polyclonal to rabbit IgG at 1/10000 dilution. Predicted band size: 31 kDa. Observed band size: 31 kDa.
product information
catalog number :
MBS7043915
products type :
Antibody
products full name :
HCCS Antibody
products short name :
[HCCS]
products name syn :
[Cytochrome c-type heme lyase, (CCHL) (EC 4.4.1.17); Holocytochrome c-type synthase; HCCS; CCHL]
other names :
[cytochrome c-type heme lyase; Cytochrome c-type heme lyase; cytochrome c-type heme lyase; holocytochrome c synthase; Holocytochrome c-type synthase]
products gene name :
[HCCS]
other gene names :
[HCCS; HCCS; MLS; CCHL; MCOPS7; LSDMCA1; CCHL; CCHL]
uniprot entry name :
CCHL_HUMAN
clonality :
Polyclonal
isotype :
IgG
host :
Rabbit
reactivity :
Human, Mouse
purity :
Antigen Affinity Purified
form :
Liquid
storage stability :
Upon receipt, aliquot and store at -20 degree C or -80 degree C. Avoid repeated freeze.
tested application :
ELISA (EIA), Western Blot (WB)
app notes :
Recommended dilution: WB:1:1000-1:5000
image1 heading :
Western Blot (WB)
other info1 :
Species: Human. Immunogen: Recombinant human Cytochrome c-type heme lyase protein (1-268AA)
other info2 :
Conjugate: Non-conjugated. Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3. Species: Human. Research Area: Cardiovascular. Santa Cruz Alternative: Potential replacement for Santa Cruz Biotechnology antibody catalog# sc-168060
products description :
Links covalently the heme group to the apoprotein of cytochrome c.
ncbi gi num :
169790851
ncbi acc num :
NP_001116080.1
ncbi gb acc num :
NM_001122608.2
uniprot acc num :
P53701
ncbi pathways :
Porphyrin And Chlorophyll Metabolism Pathway (83021); Porphyrin And Chlorophyll Metabolism Pathway (407)
ncbi summary :
The protein encoded by this gene is an enzyme that covalently links a heme group to the apoprotein of cytochrome c. Defects in this gene are a cause of microphthalmia syndromic type 7 (MCOPS7). Three transcript variants encoding the same protein have been found for this gene. [provided by RefSeq, Jan 2010]
uniprot summary :
HCCS: Links covalently the heme group to the apoprotein of cytochrome c. Defects in HCCS are a cause of microphthalmia syndromic type 7 (MCOPS7); also known as microphthalmia with linear skin defects (MLS) or MIDAS syndrome. Microphthalmia is a clinically heterogeneous disorder of eye formation, ranging from small size of a single eye TO complete bilateral absence of ocular tissues (anophthalmia). In many cases, microphthalmia/anophthalmia occurs in association with syndromes that include non-ocular abnormalities. MCOPS7 is a disorder characterized by unilateral or bilateral microphthalmia, linear skin defects in affected females, and in utero lethality for males. Skin defects are limited to the face and neck, consisting of areas of aplastic skin that heal with age to form hyperpigmented areas. Additional features in female patients include agenesis of the corpus callosum, sclerocornea, chorioretinal abnormalities, infantile seizures, congenital heart defect, mental retardation, and diaphragmatic hernia. Belongs to the cytochrome c-type heme lyase family. Protein type: Cofactor and Vitamin Metabolism - porphyrin and chlorophyll; EC 4.4.1.17; Lyase; Mitochondrial. Chromosomal Location of Human Ortholog: Xp22.3. Cellular Component: mitochondrion. Biological Process: organ morphogenesis. Disease: Microphthalmia, Syndromic 7
size1 :
0.05 mL
price1 :
120 USD
size2 :
0.1 mL
price2 :
160
more info or order :
company information
MyBioSource
P.O. Box 153308
San Diego, CA 92195-3308
San Diego, CA 92195-3308
sales@mybiosource.com
https://www.mybiosource.com1-888-627-0165
headquarters: USA
MyBioSource, LLC was orginally founded in Vancouver by three enthusiastic scientists who are passionate about providing the world with the best reagents available. Together, they form a company with a big vision known as MyBioSource. MyBioSource is now located in San Diego, California, USA.
"MyBioSource's number 1 vision is to be the world's number 1 quality reagents provider."
Our goal is to provide researchers, scientists and customers alike with a one-stop-shop for all of their reagents needs, whether it is monoclonal antibody, polyclonal antibody, recombinant protein, peptide, etc...
"MyBioSource offers the best products at unbeatable prices."
Please spend a few minutes to browse our online catalogs and see the wide range of products available. We ship our products through our shipping/distribution facility in San Diego, California, USA.
Would you like to receive email and e-newsletter from MyBioSource about new products, special offers and events? Please click here to join our Mailing List!