This webpage contains legacy information. The product is either no longer available from the supplier or has been delisted at Labome.
product summary
company name :
MyBioSource
product type :
ELISA/assay
product name :
Human Glucosidase Alpha, Acid (GaA) ELISA Kit
catalog :
MBS455608
quantity :
48-Strip-Wells
price :
375 USD
product information
catalog number :
MBS455608
products type :
ELISA Kit
products full name :
Human Glucosidase Alpha, Acid (GaA) ELISA Kit
products short name :
[Glucosidase Alpha, Acid (GaA)]
products name syn :
[LYAG; Acid Alpha-Glucosidase; Lysosomal Alpha-Glucosidase; Pompe Disease Glycogen Storage Disease Type II; Acid Maltase; Aglucosidase Alfa]
other names :
[lysosomal alpha-glucosidase preproprotein; Lysosomal alpha-glucosidase; lysosomal alpha-glucosidase; glucosidase alpha, acid; Acid maltase; Aglucosidase alfa]
products gene name :
[GaA]
other gene names :
[GAA; GAA; LYAG]
reactivity :
Human
sequence length :
952
storage stability :
For unopened kit, all reagents should be kept according to the labels on vials. The TMB Substrate, Wash Buffer, Stop Solution should be stored at 4 degree C. All others should be stored at -20 degree C.
image1 heading :
Typical Testing Data/Standard Curve (for reference only)
other info1 :
Samples: Serum, plasma, tissue homogenates, cell lysates and other biological fluids. Assay Type: Sandwich. Detection Range: 0.156-10ng/mL. Sensitivity: 0.064ng/mL
other info2 :
Intra Assay: CV<10%. Inter Assay: CV<12%
ncbi gi num :
119393891
ncbi acc num :
NP_000143.2
ncbi gb acc num :
NM_000152.4
uniprot acc num :
P10253
ncbi mol weight :
105,324 Da
ncbi pathways :
Galactose Metabolism Pathway (82931); Galactose Metabolism Pathway (292); Glucose Metabolism Pathway (1269959); Glycogen Breakdown (glycogenolysis) Pathway (1269963); Immune System Pathway (1269170); Innate Immune System Pathway (1269203); Lysosomal Glycogen Catabolism Pathway (1269964); Lysosome Pathway (99052); Lysosome Pathway (96865); Metabolic Pathways (132956)
ncbi summary :
This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2016]
uniprot summary :
Essential for the degradation of glygogen to glucose in lysosomes.
size1 :
48-Strip-Wells
price1 :
375 USD
size2 :
96-Strip-Wells
price2 :
495
size3 :
5x96-Strip-Wells
price3 :
2225
size4 :
10x96-Strip-Wells
price4 :
4320
company information
MyBioSource
P.O. Box 153308
San Diego, CA 92195-3308
sales@mybiosource.com
https://www.mybiosource.com
1-888-627-0165
headquarters: USA
MyBioSource, LLC was orginally founded in Vancouver by three enthusiastic scientists who are passionate about providing the world with the best reagents available. Together, they form a company with a big vision known as MyBioSource. MyBioSource is now located in San Diego, California, USA.

"MyBioSource's number 1 vision is to be the world's number 1 quality reagents provider."

Our goal is to provide researchers, scientists and customers alike with a one-stop-shop for all of their reagents needs, whether it is monoclonal antibody, polyclonal antibody, recombinant protein, peptide, etc...

"MyBioSource offers the best products at unbeatable prices."

Please spend a few minutes to browse our online catalogs and see the wide range of products available. We ship our products through our shipping/distribution facility in San Diego, California, USA.

Would you like to receive email and e-newsletter from MyBioSource about new products, special offers and events? Please click here to join our Mailing List!