catalog number :
MBS240020
products full name :
Rabbit Polyclonal to Human PYGL
products short name :
PYGL
products name syn :
Anti-PYGL Antibody (Internal) IHC-plus; PYGL; GPLL; Phosphorylase; glycogen liver; Phosphorylase; glycogen; liver; GSD6; Human PYGL
other names :
glycogen phosphorylase, liver form isoform 1; Glycogen phosphorylase, liver form; glycogen phosphorylase, liver form; phosphorylase, glycogen, liver
products gene name :
PYGL
other gene names :
PYGL; PYGL; GSD6
uniprot entry name :
PYGL_HUMAN
reactivity :
Dog, Gorilla, Human. Predicted Reactivity: Gibbon, Monkey (at least 90% immunogen sequence identity)
specificity :
Human PYGL. BLAST analysis of the peptide immunogen showed no homology with other human proteins.
purity :
Immunoaffinity Purified
form :
PBS, 0.1% sodium azide.
storage stability :
Long term: -70 degree C; Short term: +4 degree C
tested application :
Immunohistochemistry (IHC - Paraffin)
app notes :
IHC-P (10 ug/ml). Usage: Immunohistochemistry: was validated for use in immunohistochemistry on a panel of 21 formalin-fixed, paraffin-embedded (FFPE) human tissues after heat induced antigen retrieval in pH 6.0 citrate buffer. After incubation with the primary anti.
other info1 :
Target Species: Human. Immunogen Description: Synthetic 10 amino acid peptide from internal region of human PYGL. Percent identity with other species by BLAST analysis: Human, Gorilla, Monkey, Dog (100%); Gibbon, Marmoset, Panda (90%); Mouse, Sheep, Hamster, Horse, Rabbit (80%).
other info2 :
Immunogen Type: Synthetic peptide. Immunogen: PYGL antibody was raised against synthetic 10 amino acid peptide from internal region of human PYGL. Percent identity with other species by BLAST analysis: Human, Gorilla, Monkey, Dog (100%); Gibbon, Marmoset, Panda (90%); Mouse, Sheep, Hamster, Horse, Rabbit (80%). Antigen Modification: Internal
ncbi acc num :
NP_002854.3
ncbi gb acc num :
NM_002863.4
ncbi mol weight :
93,134 Da
ncbi pathways :
Disease Pathway 530764!!Glucose Metabolism Pathway 106199!!Glycogen Metabolism Pathway 198856!!Glycogen Breakdown (glycogenolysis) Pathway 106212!!Glycogen Storage Diseases Pathway 1127581!!Insulin Signaling Pathway 83090!!Insulin Signaling Pathway 501!!Metabolic Pathways 132956!!Metabolism Pathway 477135!!Metabolism Of Carbohydrates Pathway 106196
ncbi summary :
This gene encodes a homodimeric protein that catalyses the cleavage of alpha-1,4-glucosidic bonds to release glucose-1-phosphate from liver glycogen stores. This protein switches from inactive phosphorylase B to active phosphorylase A by phosphorylation of serine residue 15. Activity of this enzyme is further regulated by multiple allosteric effectors and hormonal controls. Humans have three glycogen phosphorylase genes that encode distinct isozymes that are primarily expressed in liver, brain and muscle, respectively. The liver isozyme serves the glycemic demands of the body in general while the brain and muscle isozymes supply just those tissues. In glycogen storage disease type VI, also known as Hers disease, mutations in liver glycogen phosphorylase inhibit the conversion of glycogen to glucose and results in moderate hypoglycemia, mild ketosis, growth retardation and hepatomegaly. Alternative splicing results in multiple transcript variants encoding different isoforms.[provided by RefSeq, Feb 2011]