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company name :
MyBioSource
product type :
cDNA
product name :
EHHADH cDNA Clone
catalog :
MBS1271840
quantity :
0.01 mg Plasmid + 0.
price :
165 USD
more info or order :
product information
catalog number :
MBS1271840
products type :
cDNA Clone
products full name :
EHHADH cDNA Clone
products short name :
EHHADH
other names :
Homo sapiens enoyl-Coenzyme A, hydratase/3-hydroxyacyl Coenzyme A dehydrogenase, mRNA; Peroxisomal bifunctional enzyme; peroxisomal bifunctional enzyme; enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase
products gene name :
EHHADH
other gene names :
EHHADH; EHHADH; LBP; ECHD; LBFP; PBFE; FRTS3; L-PBE; ECHD; PBE; PBFE
uniprot entry name :
ECHP_HUMAN
sequence length :
3811
sequence :
ATGGCCGAGTATACGCGGCTGCACAACGCCTTGGCGCTA
ATCCGCCTCCGAAACCCGCCGGTCAACGCGATCAGTACG
ACTTTACTCCGTGACATAAAAGAAGGACTACAGAAAGCT
GTAATAGACCATACAATAAAAGCCATTGTGATTTGTGGA
GCAGAGGGCAAATTTTCTGCAGGTGCTGATATTCGTGGC
TTCAGTGCTCCTAGGACATTTGGCCTTACACTGGGACAT
GTAGTAGATGAAATACAGAGAAATGAGAAGCCCGTGGTG
GCAGCAATCCAAGGCATGGCTTTCGGAGGGGGACTAGAG
CTGGCCCTGGGCTGTCACTATAGGATTGCCCACGCAGAG
GCTCAAGTTGGCTTACCAGAAGTTACACTGGGACTTCTC
CCTGGTGCAAGAGGAACCCAGCTTCTCCCCAGACTCACT
GGAGTTCCTGCTGCACTTGACTTAATTACCTCAGGAAGA
CGTATTTTAGCAGATGAAGCACTCAAGCTGGGCATTCTA
GATAAAGTTGTAAACTCAGACCCGGTTGAAGAAGCAATC
AGATTTGCTCAGAGAGTTTCAGATCAACCTCTAGAATCC
CGTAGACTCTGCAACAAGCCAATTCAGAGCTTGCCCAAC
ATGGACAGCATTTTTAGTGAGGCCCTCTTGAAGATGCGG
AGGCAGCACCCTGGGTGTCTTGCACAGGAGGCTTGTGTC
CGTGCAGTCCAGGCTGCTGTGCAGTATCCCTATGAAGTG
GGCATCAAGAAGGAGGAGGAGCTGTTTCTATATCTTTTG
CAATCAGGGCAGGCTAGAGCCCTGCAATATGCTTTCTTC
GCTGAAAGGAAAGCAAATAAGTGGTCAACTCCCTCCGGA
GCATCGTGGAAAACAGCATCAGCGCGGCCTGTCTCCTCA
GTTGGTGTTGTTGGCTTGGGAACAATGGGCCGAGGCATT
GTCATTTCTTTTGCAAGGGCCAGGATTCCTGTGATTGCT
GTAGACTCGGACAAAAACCAGCTAGCAACTGCAAACAAG
ATGATAACCTCTGTCTTGGAAAAAGAAGCCTCCAAAATG
CAACAGAGCGGCCACCCTTGGTCAGGACCAAAACCCAGG
TTAACTTCATCTGTGAAGGAGCTTGGTGGTGTAGATTTA
GTCATTGAAGCAGTATTTGAGGAAATGAGCCTGAAGAAG
CAGGTCTTTGCTGAACTCTCAGCTGTGTGCAAACCAGAA
GCATTTTTGTGCACTAATACTTCAGCCCTGGATGTTGAT
GAGATTGCTTCTTCCACTGATCGTCCTCACTTGGTCATT
GGCACCCACTTCTTTTCGCCAGCTCATGTCATGAAGTTG
TTAGAGGTTATTCCCAGCCAATACTCTTCCCCCACTACC
ATTGCCACTGTTATGAACTTATCAAAAAAGATTAAAAAG
ATTGGAGTCGTTGTAGGCAACTGTTTTGGATTTGTGGGG
AATCGAATGTTGAATCCTTACTACAATCAGGCATATTTC
TTGTTAGAAGAAGGCAGCAAACCAGAGGAGGTAGATCAG
GTGCTGGAAGAGTTTGGTTTTAAAATGGGACCTTTTAGA
GTGTCTGATCTTGCTGGGTTGGATGTGGGCTGGAAATCT
AGAAAGGGGCAAGGTCTTACTGGACCTACATTGCTTCCA
GGAACTCCTGCCCGAAAAAGGGGTAATAGGAGGTACTGC
CCAATTCCTGATGTGCTCTGTGAATTAGGACGATTTGGC
CAGAAGACAGGTAAGGGTTGGTATCAATATGACAAGCCA
TTGGGTAGGATTCACAAACCTGATCCCTGGCTTTCCAAA
TTCCTATCACGGTATAGAAAAACCCATCACATTGAACCA
CGTACCATTAGCCAGGATGAGATCCTTGAACGCTGCTTA
TATTCACTTATCAATGAAGCATTCCGTATCTTGGGAGAA
GGGATAGCTGCTAGCCCAGAGCACATTGATGTTGTCTAT
TTACATGGATATGGATGGCCAAGGCACAAGGGCGGGCCC
ATGTTCTATGCTTCCACAGTTGGGTTGCCCACAGTTCTA
GAGAAATTGCAGAAATATTACAGGCAGAACCCTGATATT
CCCCAACTGGAGCCAAGTGACTATCTAAAAAAACTGGCT
TCTCAGGGAAACCCTCCCCTGAAAGAATGGCAAAGCTTG
GCAGGCTCCCCTAGCAGTAAATTGTGA
other info1 :
Vector: Please Inquire
ncbi gi num :
25058572
ncbi acc num :
BC038948
ncbi mol weight :
69,154 Da
ncbi pathways :
Butanoate Metabolism Pathway (83007); Butanoate Metabolism Pathway (391); Fatty Acid Metabolism Pathway (82935); Fatty Acid Metabolism Pathway (296); Lysine Degradation Pathway (82956); Lysine Degradation Pathway (320); Lysine Degradation, Lysine = Saccharopine = Acetoacetyl-CoA Pathway (413352); Lysine Degradation, Lysine = Saccharopine = Acetoacetyl-CoA Pathway (468225); Malonate Semialdehyde Pathway, Propanoyl-CoA = Acetyl-CoA (413478); Malonate Semialdehyde Pathway, Propanoyl-CoA = Acetyl-CoA (468206)
ncbi summary :
The protein encoded by this gene is a bifunctional enzyme and is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of the encoded protein contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in this gene are a cause of peroxisomal disorders such as Zellweger syndrome. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Oct 2009]
uniprot summary :
EHHADH: 2 isoforms of the human protein are produced by alternative splicing. Protein type: Lyase; Amino Acid Metabolism - valine, leucine and isoleucine degradation; Mitochondrial; Other Amino Acids Metabolism - beta-alanine; Oxidoreductase; Isomerase; EC 1.1.1.35; Amino Acid Metabolism - lysine degradation; EC 4.2.1.17; Secondary Metabolites Metabolism - limonene and pinene degradation; Carbohydrate Metabolism - propanoate; Lipid Metabolism - fatty acid; EC 5.3.3.8; Amino Acid Metabolism - tryptophan; Carbohydrate Metabolism - butanoate. Chromosomal Location of Human Ortholog: 3q26.3-q28. Cellular Component: peroxisomal matrix; peroxisome. Molecular Function: 3-hydroxyacyl-CoA dehydrogenase activity; enzyme binding; long-chain-enoyl-CoA hydratase activity; protein binding; receptor binding. Biological Process: cellular lipid metabolic process; internal protein amino acid acetylation. Disease: Fanconi Renotubular Syndrome 3
size1 :
0.01 mg Plasmid + 0.2 mL Glycerol-Stock
price1 :
165 USD
more info or order :
company information
MyBioSource
P.O. Box 153308
San Diego, CA 92195-3308
sales@mybiosource.com
https://www.mybiosource.com
1-888-627-0165
headquarters: USA
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