Published Application/Species/Sample/Dilution | Reference |
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- immunohistochemistry - frozen section; human; fig 1
| Janghra N, Morgan J, Sewry C, Wilson F, Davies K, Muntoni F, et al. Correlation of Utrophin Levels with the Dystrophin Protein Complex and Muscle Fibre Regeneration in Duchenne and Becker Muscular Dystrophy Muscle Biopsies. PLoS ONE. 2016;11:e0150818 pubmed publisher
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- western blot; mouse; fig 1
| Ferry A, Parlakian A, Joanne P, Fraysse B, Mgrditchian T, Roy P, et al. Mechanical Overloading Increases Maximal Force and Reduces Fragility in Hind Limb Skeletal Muscle from Mdx Mouse. Am J Pathol. 2015;185:2012-24 pubmed publisher
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| Ljubicic V, Jasmin B. Metformin increases peroxisome proliferator-activated receptor γ Co-activator-1α and utrophin a expression in dystrophic skeletal muscle. Muscle Nerve. 2015;52:139-42 pubmed publisher
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- immunohistochemistry; rhesus macaque; loading ...; fig 8c
- western blot; rhesus macaque; loading ...; fig 8a
| Chicoine L, Rodino Klapac L, Shao G, Xu R, Bremer W, Camboni M, et al. Vascular delivery of rAAVrh74.MCK.GALGT2 to the gastrocnemius muscle of the rhesus macaque stimulates the expression of dystrophin and laminin ?2 surrogates. Mol Ther. 2014;22:713-24 pubmed publisher
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| Mavillard F, Madruga Garrido M, Rivas E, Servián Morilla E, Ávila Polo R, Marcos I, et al. NOVEL intronic CAPN3 Roma mutation alters splicing causing RNA mediated decay. Ann Clin Transl Neurol. 2019;6:2328-2333 pubmed publisher
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| Sánchez L, Beltran E, De Stefani A, Guo L, Shea A, Shelton G, et al. Clinical and genetic characterisation of dystrophin-deficient muscular dystrophy in a family of Miniature Poodle dogs. PLoS ONE. 2018;13:e0193372 pubmed publisher
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| Carlson C, Moore S, Mathews K. Dystrophinopathy muscle biopsies in the genetic testing ERA: One center's data. Muscle Nerve. 2018;: pubmed publisher
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| Packer R, Logan M, Guo L, Apte S, Bader H, O Brien D, et al. Clinical Phenotype of Musladin-Lueke Syndrome in 2 Beagles. J Vet Intern Med. 2017;31:532-538 pubmed publisher
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| Al Sarraj S, King A, Cleveland M, Pradat P, Corse A, Rothstein J, et al. Mitochondrial abnormalities and low grade inflammation are present in the skeletal muscle of a minority of patients with amyotrophic lateral sclerosis; an observational myopathology study. Acta Neuropathol Commun. 2014;2:165 pubmed publisher
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| Larcher T, Lafoux A, Tesson L, Remy S, Thepenier V, François V, et al. Characterization of dystrophin deficient rats: a new model for Duchenne muscular dystrophy. PLoS ONE. 2014;9:e110371 pubmed publisher
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| Amirouche A, Tadesse H, Miura P, Belanger G, Lunde J, Cote J, et al. Converging pathways involving microRNA-206 and the RNA-binding protein KSRP control post-transcriptionally utrophin A expression in skeletal muscle. Nucleic Acids Res. 2014;42:3982-97 pubmed publisher
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| Chandrasekharan K, Yoon J, Xu Y, DeVries S, Camboni M, Janssen P, et al. A human-specific deletion in mouse Cmah increases disease severity in the mdx model of Duchenne muscular dystrophy. Sci Transl Med. 2010;2:42ra54 pubmed publisher
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| Guerron A, Rawat R, Sali A, Spurney C, Pistilli E, Cha H, et al. Functional and molecular effects of arginine butyrate and prednisone on muscle and heart in the mdx mouse model of Duchenne Muscular Dystrophy. PLoS ONE. 2010;5:e11220 pubmed publisher
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| Gambardella S, Rinaldi F, Lepore S, Viola A, Loro E, Angelini C, et al. Overexpression of microRNA-206 in the skeletal muscle from myotonic dystrophy type 1 patients. J Transl Med. 2010;8:48 pubmed publisher
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| Mattei E, Corbi N, Di Certo M, Strimpakos G, Severini C, Onori A, et al. Utrophin up-regulation by an artificial transcription factor in transgenic mice. PLoS ONE. 2007;2:e774 pubmed
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| Burkin D, Wallace G, Nicol K, Kaufman D, Kaufman S. Enhanced expression of the alpha 7 beta 1 integrin reduces muscular dystrophy and restores viability in dystrophic mice. J Cell Biol. 2001;152:1207-18 pubmed
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