This webpage contains legacy information. The product is either no longer available from the supplier or has been delisted at Labome.
product summary
company name :
Invitrogen
other brands :
NeoMarkers, Lab Vision, Endogen, Pierce, BioSource International, Zymed Laboratories, Caltag, Molecular Probes, Research Genetics, Life Technologies, Applied Biosystems, GIBCO BRL, ABgene, Dynal, Affinity BioReagents, Nunc, Invitrogen, NatuTec, Oxoid, Richard-Allan Scientific, Arcturus, Perseptive Biosystems, Proxeon, eBioscience
product type :
antibody
product name :
NAGA Polyclonal Antibody
catalog :
PA5-47863
quantity :
100 ug
price :
US 474.00
clonality :
polyclonal
host :
domestic sheep
conjugate :
nonconjugated
reactivity :
human
application :
western blot, immunocytochemistry
product information
Product Type :
Antibody
Product Name :
NAGA Polyclonal Antibody
Catalog # :
PA5-47863
Quantity :
100 ug
Price :
US 474.00
Clonality :
Polyclonal
Purity :
Antigen affinity chromatography
Host :
Sheep
Reactivity :
Human
Applications :
Immunocytochemistry: 5-15 ug/mL, Western Blot: 1 ug/mL
Species :
Human
Isotype :
IgG
Storage :
-20 C, Avoid Freeze/Thaw Cycles
Description :
NAGA (N-acetylgalactosaminidase, alpha), also known as alpha-galactosidase B or GALB, is a 411 lysosomal protein belonging to the glycosyl hydrolase 27 family that may exist as a homodimer and plays a critical role in glycolipid breakdown. NAGA encodes alpha-N-acetylgalactosaminidase, a lysosomal enzyme, which cleaves alpha-N-acetylgalactosaminyl groups from glycoconjugates. Mapping to human chromosome 22q13. 2, NAGA defects are the cause of an autosomal recessive disorder with three phenotypes, known as Schindler disease (types I, II and III) or NAGA deficiency (types I, II and III). Characterized by neurologic manifestations that range in severity, Schindler disease type I is the most severe form, followed by type III, which may have mild-to-moderate effects. Schindler disease type II, also known as Kanzaki disease, is characterized by mild intellectual impairment and angiokeratoma corporis diffusum.
Immunogen :
CHO-derived recombinant human alpha-N-acetylgalactosaminidase/NAGA Leu18-Gln411
Format :
Lyophilized
Applications w/Dilutions :
Immunocytochemistry: 5-15 ug/mL, Western Blot: 1 ug/mL
Aliases :
Acetylgalactosaminidase, alpha-N- (alpha-galactosidase B); alpha-galactosidase B; Alpha-N-acetylgalactosaminidase; D22S674; EC 3.2.1; EC 3.2.1.49; galactosidasealphaB; galactosidase-alphaB; GALB; N-acetyl galactosaminidase, alpha; N-acetylgalactosaminidase, alpha-; Naga
company information
Invitrogen
Thermo Fisher Scientific
81 Wyman Street
Waltham, MA USA 02451
https://www.thermofisher.com
800-678-5599
headquarters: USA