This webpage contains legacy information. The product is either no longer available from the supplier or has been delisted at Labome.
product summary
company name :
Invitrogen
other brands :
NeoMarkers, Lab Vision, Endogen, Pierce, BioSource International, Zymed Laboratories, Caltag, Molecular Probes, Research Genetics, Life Technologies, Applied Biosystems, GIBCO BRL, ABgene, Dynal, Affinity BioReagents, Nunc, Invitrogen, NatuTec, Oxoid, Richard-Allan Scientific, Arcturus, Perseptive Biosystems, Proxeon, eBioscience
product type :
antibody
product name :
GBE1 Polyclonal Antibody
catalog :
PA5-26515
quantity :
400 uL
price :
US 474.00
clonality :
polyclonal
host :
domestic rabbit
conjugate :
nonconjugated
reactivity :
human, mouse
application :
western blot, immunocytochemistry
citations: 1
Reference
Fanjul Fernandez M, Brown N, Hickey P, Diakumis P, Rafehi H, Bozaoglu K, et al. A family study implicates GBE1 in the etiology of autism spectrum disorder. Hum Mutat. 2022;43:16-29 pubmed publisher
product information
Product Type :
Antibody
Product Name :
GBE1 Polyclonal Antibody
Catalog # :
PA5-26515
Quantity :
400 uL
Price :
US 474.00
Clonality :
Polyclonal
Purity :
Antigen affinity chromatography, Protein A
Host :
Rabbit
Reactivity :
Human, Mouse
Applications :
Immunocytochemistry: 1:10-1:50, Western Blot: 1:1,000
Species :
Human, Mouse
Isotype :
IgG
Storage :
Store at 4 C short term. For long term storage, store at -20 C, avoiding freeze/thaw cycles.
Description :
GBE1 is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease).
Immunogen :
KLH conjugated synthetic peptide between 527-556 amino acids from the central region of human GBE1
Format :
Liquid
Applications w/Dilutions :
Immunocytochemistry: 1:10-1:50, Western Blot: 1:1,000
Aliases :
1,4-alpha-glucan-branching enzyme; 2310045H19Rik; 2810426P10Rik; amylo-(1,4 to 1,6) transglucosidase; amylo-(1,4 to 1,6) transglycosylase; APBD; Brancher enzyme; D16Ertd536e; GBE; GBE1; glucan (1,4-alpha-), branching enzyme 1; glycogen branching enzyme; glycogen-branching enzyme; GSD4
company information
Invitrogen
Thermo Fisher Scientific
81 Wyman Street
Waltham, MA USA 02451
https://www.thermofisher.com
800-678-5599
headquarters: USA