TRPML1 Polyclonal Antibody | Invitrogen OSM00035W product information

This webpage contains legacy information. The product is either no longer available from the supplier or has been delisted at Labome.

product summary

company name :

Invitrogen

other brands :

NeoMarkers, Lab Vision, Endogen, Pierce, BioSource International, Zymed Laboratories, Caltag, Molecular Probes, Research Genetics, Life Technologies, Applied Biosystems, GIBCO BRL, ABgene, Dynal, Affinity BioReagents, Nunc, Invitrogen, NatuTec, Oxoid, Richard-Allan Scientific, Arcturus, Perseptive Biosystems, Proxeon, eBioscience

product type :

antibody

product name :

TRPML1 Polyclonal Antibody

catalog :

OSM00035W

quantity :

100 µL

price :

US 425

clonality :

polyclonal

host :

domestic sheep

conjugate :

nonconjugated

reactivity :

human

application :

western blot, immunohistochemistry

product information

Product Type :

Antibody

Product Name :

TRPML1 Polyclonal Antibody

Catalog # :

OSM00035W

Quantity :

100 µL

Price :

US 425

Clonality :

Polyclonal

Host :

Sheep

Reactivity :

Human

Applications :

Immunohistochemistry: 1:300-1:2,000, Western Blot: 1:300-1:2,000

Species :

Human

Isotype :

IgG

Storage :

Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles. Glycerol (1:1) may be added for added stability.

Description :

Defects in Mucolipin-1 are the cause of mucolipidosis type IV (MLIV), also known as sialolipidosis. MLIV is an autosomal recessive lysosomal storage disorder characterized by severe psychomotor retardation and ophthalmologic abnormalities, including corneal opacity, retinal degeneration and strabismus. Storage bodies of lipids and water-soluble substances are seen by electron microscopy in almost every cell type of the patients. Most patients are unable to speak or walk independently and reach a maximal developmental level of 1-2 years. All patients have constitutive achlorhydia associated with a secondary elevation of serum gastrin levels.

Immunogen :

A synthetic peptide from human Mucolipin 1

Format :

Lyophilized

Applications w/Dilutions :

Immunohistochemistry: 1:300-1:2,000, Western Blot: 1:300-1:2,000

Aliases :

2210015I05Rik; MCLN1; Mcoln1; MCOLN1 mucolipin 1; MG-2; MGC7172; ML1; ML4; MLIV; MST080; MSTP080; Mucolipidin; mucolipidosis type IV protein; mucolipin 1; mucolipin-1; Transient receptor potential channel mucolipin 1; Transient receptor potential-mucolipin 1; TRPML1; TRP-ML1; TRPM-L1